What is Storiform-Pleomorphic Tumour?
Storiform-pleomorphic tumour is a rare and complex form of soft tissue sarcoma. The term “storiform” refers to the unique ‘mat-like’ arrangement of tumour cells when observed under a microscope, while “pleomorphic” denotes the presence of cells of varying shapes and sizes. These tumours often originate in connective or soft tissue, and their behaviour can range from relatively indolent (slow-growing) to highly aggressive.
Symptoms
The symptoms of a storiform-pleomorphic tumour largely depend on the tumour’s size and location but typically include:
- A palpable lump or swelling in the affected area.
- Pain or discomfort, particularly if the tumour compresses nearby nerves or muscles.
- The restricted movement if the tumour is located near joints.
- In more aggressive cases, systemic symptoms like weight loss, fatigue, and malaise might occur.
Disease Aetiology (Causes)
The exact cause of storiform-pleomorphic tumours is not fully understood. Genetic mutations, environmental factors, and a history of radiation exposure are considered potential contributing factors.
Diagnosis
Diagnosing a storiform-pleomorphic tumour involves:
- Physical Examination: To assess any visible or palpable lumps.
- Imaging Studies: MRI, CT scans, or ultrasound to evaluate the tumour’s size, depth, and impact on surrounding tissues.
- Biopsy: A tissue sample is crucial for a definitive diagnosis, involving histopathological examination.
Treatment
Treatment for storiform-pleomorphic tumours may include:
- Surgery: The primary treatment approach, aims to remove the tumour with clear margins.
- Radiation Therapy: Often used post-surgery, especially if there’s a high risk of recurrence or if complete removal isn’t possible.
- Chemotherapy: May be considered in aggressive cases or if the tumour has metastasized.
- Targeted Therapy: In cases where specific genetic mutations are present, targeted therapies can be effective.
What support can we give for Storiform-Pleomorphic Tumour?
Storiform-Pleomorphic Tumour is a rare cancer, meaning it is not as well-known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Storiform-Pleomorphic Tumour, we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
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Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways:
