What is Primary Cardiac Leiomyosarcoma?
Primary cardiac leiomyosarcoma is a very rare type of heart cancer that arises from the smooth muscle cell tissues of the heart. It accounts for approximately 0.001% to 0.03% of all cancers of the heart. It tends to invade the underneath tissues of the heart, lungs, and breast. It grows rapidly with the tendency to spread to the other distant parts of the body, thus showing a poor prognosis.
There is no well-known cause, however, certain hereditary and genetic mutations are considered responsible for the development of primary cardiac Leiomyosarcoma.
Signs and Symptoms
The patient may suffer from the following signs and symptoms. These are
- Difficulty in breathing
- Pain in the chest
- Irregular heartbeat
- Heart failure
- Pulmonary edema (accumulation of fluids in the lungs)
- Low blood pressure
The following investigations help diagnose the disease and its extent. These are
- Complete blood count ( CBC)
- Electrocardiogram (EKG OR ECG)
- CT-scan and MRI
- Immunohistochemical staining
- Chest X-Ray
- Tumour biopsy
- The selection of suitable treatment depends upon multiple factors like the size, number, and location of the tumor. Surgical removal of the tumor along with chemotherapy and radiation therapy is the main treatment option.
What Support can we Give for Primary Cardiac Leiomyosarcoma?
Primary Cardiac Leiomyosarcoma is rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Primary Cardiac Leiomyosarcoma, we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways: