What is Peritoneal Pseudomyxoma?
Peritoneal Pseudomyxoma or Pseudomyxoma peritoneum is a rare type of cancer that originates from the epithelial cells of the appendix as a small growth called a polyp. The cancerous cells from the appendicular polyps then spread to the peritoneal tissues that make the lining of the abdominal cavity. These cancerous cells produce mucus in the appendix sometimes also called appendiceal mucinous tumors. Peritoneal pseudomyxoma does not spread to any other parts of the body via the lymphatic or blood systems. In the meantime, it spread by peritoneal fluid flow from the appendix cancer cells to the entire abdomen. These cells adhere to the peritoneum (abdominal cavity) at a specific location and begin to produce mucus, which gathers inside the abdomen and begins to cause symptoms.
Disease Causes
There is no well-known cause, however certain hereditary and genetic mutations along with the inflammation of the appendix a potential risk factors for the development of peritoneal pseudomyxoma or pseudomyxoma peritonei. Signs and symptoms The patient may suffer from the following signs and symptoms. These are
Signs and Symptoms
The patient may suffer from the following signs and symptoms. These are
- Pain in the abdomen
- Distension of the abdomen
- Nausea
- Vomiting
- Loss of appetite (hunger)
- Constipation
- Unexplained weight loss
- Hernia (bulge of any abdominal organ from the weak muscle of the abdomen or groin)
- Constant fever
- Excessive sweating at night
- Constant fatigue
Diagnosis
The following diagnostic tests and procedures can be used to make a diagnosis. These are
- USG of the abdomen and Pelvis
- Endoscopic examination of the anus, rectum, and large intestine. Endoscopy is a procedure that allows the doctor to visualize the internal organs of the body directly through the endoscope.
- Computed tomography (CT-abdomen and pelvis), PET-scan.
- Biopsy of the lesion/tumor and histopathological examination
- Blood test for CA-125 (CA-125 is a cancer marker that can indicate the presence of some cancers in the body if its level is greater).
- Barium meal USG to see upper and lower gastrointestinal tract (esophagus, stomach, intestine, and rectum)
- Biopsy of the tumor cells
Treatment
Surgical removal of the tumor is the main treatment option. Other treatment options are chemotherapy and radiation therapy.
What Support can we Give for Peritoneal Pseudomyxoma?
Peritoneal Pseudomyxoma is rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Peritoneal Pseudomyxoma, we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways: