What is Mediastinal Lymphangioma?
Mediastinal lymphangioma is a rare type of benign tumour that develops due to the developmental abnormality of the vascular and lymphatic system of that specific area of origin. These types of tumours can originate from anywhere along with the lymphatic system but usually originate from the lymphatic system of the neck region.
What is the Lymphatic System?
The lymphatic system is a large network of lymphatic vessels, lymph nodes, and lymphatic organs. These lymph vessels run throughout the body and help drain tissues, transport fat, and destroy harmful viruses and bacteria that attack the body.
What is Mediastinum?
The mediastinum is a space in the thorax that contains the heart, thymus gland, portions of the esophagus trachea, and other structures.
Mediastinal lymphangiomas usually develop in children around 2 years of age in the neck region. It is usually rare in adults, but a few cases have been reported in adults.
There is no well-known cause, however, certain hereditary and genetic mutations are considered responsible for the development of benign lymphangioma of the mediastinum.
Signs and Symptoms
The patient may suffer from the following signs and symptoms. These are
- Difficulty in breathing
- Pain in the chest
- Unexplained weight loss
The following diagnostic tests and procedures can be used to make a diagnosis. These are;
- Imaging techniques like Chest X-ray, CT-scan, MRI, and PET scan to see the site, size, and extent of the tumour.
- Tumour biopsy (tumour biopsy to remove a small sample of tissue for histopathological examination)
- Sputum cytology
- USG-guided fine needle aspiration cytology
Surgical resection of the tumour is the main treatment.
What Support can we Give for Mediastinal Lymphangioma?
Mediastinal Lymphangioma is rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Mediastinal Lymphangioma, we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways: