What is Clear Cell Sarcoma of the Kidney?
Clear Cell Sarcoma of the Kidney is a rare and aggressive type of kidney cancer that mainly affects young children, typically between ages 1 and 4. It differs from the more common Wilms tumour due to its unique cancer cell structure.
Causes
The exact cause is unknown, but genetic changes may play a role. In rare cases, it is associated with certain birth conditions, like Beckwith-Wiedemann syndrome.
Signs and Symptoms
Symptoms often include:
- Abdominal swelling or a palpable lump
- Blood in the urine
- Fever
- Occasionally high blood pressure
In advanced cases, the cancer may spread to bones or lungs.
Diagnosis
Diagnosis typically includes:
- Imaging tests (ultrasound, CT scan, MRI) to locate and evaluate the tumour
- Biopsy or examination during kidney surgery to confirm the diagnosis
Treatment
Standard treatment involves:
- Surgical removal of the affected kidney (nephrectomy)
- Follow-up chemotherapy to reduce recurrence or spread
- Radiation therapy may be considered if there’s metastasis or incomplete removal
Prognosis
The outlook varies:
- For localised cases, the five-year survival rate is about 70%
- Prognosis worsens if the cancer has spread, underscoring the importance of early detection
You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways:
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