What is Papillary Renal Cell Carcinoma?
Papillary renal cell carcinoma is a slow-growing cancer of the kidney tubules that originates from the epithelial layer of the kidney. These tubules help to remove waste products from the blood, which is excreted in the urine. The 5-year survival rate is 82-90%. Although it usually develops in one kidney, it can develop in both kidneys or as multiple tumours.
Disease Epidemiology
Papillary renal cell carcinoma type 1 accounts for approximately 15% of all renal cell carcinomas. The average age at the development of the disease is 50 to 60 years. It is slightly more common in females than males.
Disease Etiology (Causes)
There is no well-known cause; however, it is associated with a genetic disease named Birt-Hogg-Dub syndrome.
Signs and Symptoms
In most cases, there are no symptoms, and cancer or renal tumor is detected on the occasional radiologic examination. In advance cases, the patient may develop the following signs and symptoms. These are
- Pain in the loin
- Passage of blood or blood particles in the urine
- A palpable mass in the loin or abdomen
- Unexplained weight loss
- Night sweats
- High blood pressure
- Fever
- Lethargy
Diagnosis
The following diagnostic tests and procedures can be used to make a diagnosis. These are
- Imaging techniques like CT-abdomen and pelvis, USG abdomen and pelvis, MRI, CT-chest, and X-ray to assess the site, size, extent, and distant metastasis of the tumour.
- Renal arteriography ( Ultrasonography of the main artery of the kidney)
- Venography
- CT-scan and MRI brain to detect the distant metastasis of the tumour
Treatment
Surgical resection (surgical removal of the tumour) is the main treatment option.
What Support can we Give for Papillary Renal Cell Carcinoma Type-1?
Papillary Renal Cell Carcinoma Type-1 is rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Papillary Renal Cell Carcinoma Type-1 we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
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Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways: