What is Mediastinal Lymphangiopericytoma?
Mediastinal lymphangiopericytoma is a rare type of benign tumour that develops from the excessive multiplication or division of smooth muscle cells, endothelial cells of the lymphatic system or cells of the lymph nodes. These are more common in females. Mediastinal lymphangiopericytoma can develop in children and adults. Although it is a non-cancerous tumour if it is left untreated can produce pressure symptoms on the heart, blood vessels and lungs, it can also spread to the heart and major blood vessels of the heart.What is Mediastinum?
The mediastinum is a space in the thorax that contains the heart, thymus gland, portions of the esophagus trachea, and other structures.Disease Causes
There is no well-known cause, however, certain hereditary and genetic mutations are considered responsible for the development of mediastinal lymphangiopericytoma.Signs and Symptoms
The patient may suffer from the following signs and symptoms. These are- Cough
- Difficulty in breathing
- Pain in the chest
- Unexplained weight loss
- Fever
- Coughing up blood in advanced and large lymphangiopericytoma tumour
Diagnosis
The following diagnostic tests and procedures can be used to make a diagnosis. These are;- Imaging techniques like Chest X-ray, CT-scan, MRI, and PET scan to see the site, size, and extent of the tumour.
- Tumour biopsy (tumour biopsy to remove a small sample of tissue for histopathological examination)
- Sputum cytology
- USG-guided fine needle aspiration cytology
Treatment
Surgical resection of the tumour is the main treatment.What Support can we Give for Mediastinal Lymphangiopericytoma?
Mediastinal Lymphangiopericytoma is rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Mediastinal Lymphangiopericytoma, we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways:Donations — Without a Ribbon is grateful when we receive every donation. Giving to Without a Ribbon helps us to provide ongoing support, organise the annual gathering and subsidise the costs of our Warriors attending these conferences.
Sponsorship — If you wish to sponsor our charity, please contact us using this form.
Volunteering — We are always looking for volunteers to help with different aspects of running our charity. So, if you are looking for volunteer work, please feel free to contact us.
