What is the Primary Adenoid Cystic Carcinoma of the Lungs?
Primary Adenoid cystic carcinoma of the lungs is a rare type of cancer in the respiratory tract and lungs. Primary adenoid cystic carcinoma of the lungs has the tendency to spread to other distant parts of the body. The most frequent sites of the spread of the tumour are lymph nodes, spleen, liver, kidneys and bones. It is a very rare type of cancer and accounts for approximately 0.04%-0.2% of all primary lung tumours. It shows a good prognosis (likely course of the disease) with 5-10 years survival rate ranging from 92-70%.
Disease Etiology (Causes)
There is no definite well-known cause. However, certain genetic mutations (alteration or deletion in normal genes or chromosomes) and long-term cigarette smoking are potential risk factors for the development of primary adenoid cystic carcinoma lung. General respiratory symptoms of primary adenoid cystic carcinoma of lung:
- Persistent cough
- Dyspnea (shortness of breath or difficulty in breathing)
- Chest pain that worsens with coughing, laughing and breathing deeply
- Coughing up blood
- Wheezing without having an asthma history
- Clubbing of the fingers and nails (A physical sign characterized by a bulging extension at the ends of one or more fingers or toes).
The following are the general B symptoms (systemic symptoms) of primary adenoid cystic carcinoma lungs when it spreads to other organs of the body. These are:
- Fever
- Fatigue
- Night sweats
- Weight loss
- Bone pains
Diagnosis
The following diagnostic tests and procedures can be used to make a diagnosis. These are;
- Imaging techniques like Chest X-ray, CT-scan, MRI, and PET scan to see the site, size, and extent of the tumour.
- Tumour biopsy ( lung tumour biopsy to remove a small sample of lung tissue for histopathological examination)
- Sputum cytology
- USG-guided fine needle aspiration cytology
Treatment options include surgical resection of the tumour, Chemotherapy, Radiotherapy, targeted therapy, and immunotherapy. Surgery is the main option, all patients with stages I adenocarcinoma lung should undergo surgical resection of the tumour (complete removal of the tumour along with the removal of some surrounding healthy tissues). Chemotherapy and radiotherapy should be considered in advanced cases of cancer.
What Support can we Give for Primary Adenoid Cystic Carcinoma of the Lungs?
Primary Adenoid Cystic Carcinoma of the Lungs is a rare cancer, meaning it is not as well-known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Primary Adenoid Cystic Carcinoma of the Lungs, we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways:
