What is Neurofibrosarcoma of the Vulva?
Neurofibrosarcoma of the vulva is an extremely rare type of soft tissue sarcoma. It is also known as malignant peripheral nerve sheath tumour (MPNST) of the Vulva. These tumours typically originate from cells that surround and protect our nerves. When it occurs in the vulva, it involves the external female genitalia, including the clitoris, the labia, and the opening of the vagina. This type of cancer originates from Schwann cells, which are cells that generate the protective myelin sheath that covers peripheral nerves. When these cells become cancerous, they can form tumours that put pressure on and damage the nerves.Symptoms
Symptoms of neurofibrosarcoma of the vulva can include:- A lump or mass in the vulvar region
- Pain or discomfort in the vulva
- Unusual bleeding or discharge
- Changes in the skin of the vulva
Disease Aetiology (Causes)
The exact cause of neurofibrosarcoma of the vulva is unknown. It may develop sporadically or in association with Neurofibromatosis type 1, a genetic condition that causes tumours to grow along nerves.Diagnosis
Diagnosis of neurofibrosarcoma of the vulva typically involves:- Detailed medical history and physical examination
- Biopsy of the suspicious area to examine the cells under a microscope
- Imaging tests such as ultrasound, CT scan, or MRI to determine the extent and spread of the cancer
Treatment
The treatment for neurofibrosarcoma of the vulva often includes:- Surgery: The main treatment usually involves the removal of the tumour and a margin of healthy tissue surrounding it.
- Radiation therapy: This can be used post-surgery to kill any remaining cancer cells, or as a primary treatment if surgery is not an option.
- Chemotherapy: Given the aggressive nature of neurofibrosarcomas, chemotherapy may be used, particularly if the cancer has spread to other parts of the body.
What Support can we Give for Neurofibrosarcoma of the Vulva?
Neurofibrosarcoma of the Vulva is rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Neurofibrosarcoma of the Vulva, we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways:Donations — Without a Ribbon are grateful when we receive every donation. Giving to Without a Ribbon helps us to provide ongoing support, organise the annual gathering and subsidise the costs of our Warriors attending these conferences.
Sponsorship — If you wish to sponsor our charity, please contact us using this form.
Volunteering — We are always looking for volunteers to help with different aspects of running our charity. So, if you are looking for volunteer work, please feel free to contact us.
