What is Nasopharyngeal Adenoid Cystic Carcinoma?
Adenoid cystic carcinoma of the nasopharynx is a rare, slowly growing aggressive tumour with a high tendency to relapse. It also tends to metastasize (spread to other parts of the body from its place of origin) to other parts of the body, such as the lungs and bones. Common sites for the disease are the parotid glands, the soft and hard palate, the submandibular or salivary glands, and the paranasal glands. These glands are present in the head, face, and neck regions.
Disease Epidemiology
It is a rare tumor that accounts for approximately 1% of all head and neck cancers. The five-year survival rate is approximately 89%. It can develop at any age, but the average age for developing this tumor is 50 years.
Disease Etiology (Causes)
There is no well-known cause; however, certain genetic mutations are thought to be responsible for the development of adenoid cystic carcinoma of the nasopharynx.
Signs and Symptoms
- Obstruction or blockage of the nose
- Bloodstained phlegm
Diagnosis
The following diagnostic tests and procedures can be used to make a diagnosis. These are
- Imaging tests such as X-Ray, CT-scan (computerized tomography), PET-scan (Positron emission tomography) help detect the site, size, and location of the tumor.
- Complete blood count (CBC)
- Tumor biopsy and histopathological examination
- Nasopharyngolaryngoscopy (A camera device that is inserted into the mouth and throat to visualize the mouth, throat and larynx to detect any disease).
Treatment
Complete surgical resection (surgical removal of the tumor along with some surrounding healthy tissues) of the tumor along with radiation therapy is the main treatment option. Nasopharyngeal adenoid cystic carcinoma is not much responsive to the chemotherapy.
What Support can we Give for Nasopharyngeal Adenoid Cystic Carcinoma?
Nasopharyngeal adenoid cystic carcinoma is rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Nasopharyngeal adenoid cystic carcinoma we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways:
