What is a Malignant Triton Tumour?
Malignant triton tumour is a high-grade tumour and the subtype of malignant peripheral nerve sheath tumour. Malignant Triton tumour generally arises from the distant part of the nerves of the head, neck, arms, legs, chest, and abdomen.
What is a malignant peripheral nerve sheath tumour?
A malignant peripheral nerve sheath tumour (MPNST) is a type of connective tissue (tissues that bind, separate, or support other tissues or organs) cancer that surrounds the nerves. It is a high-grade tumour and shows a poor prognosis (likely course of the disease). The 5-year survival rate with treatment is 10-14%.
What is a high-grade tumour?
A high-grade tumour is a tumour that grows rapidly and spreads to other parts of the body from where it originated.
Disease Causes
There is no well-known cause.
Disease Epidemiology
Malignant triton tumour accounts for approximately 5% of all malignant peripheral nerve sheath tumours (MPNST). It is equally common in both males and females. It can occur at any age but the peak age for the occurrence of the disease is 30 years.
Signs and symptoms
The patient may suffer from the following signs and symptoms. These are
- Malignant Triton tumour generally arises from the distant part of the nerves of the head, neck, arms, legs, chest, and abdomen.
- In very rare cases malignant triton tumours can originate from the brain, heart, lungs, spleen, liver, and buttocks.
- Slowly growing solid mass which is usually painless usually develops at the shoulder, arms, legs, chest, abdomen, or head, and neck region.
DIAGNOSIS AND TREATMENT
Diagnostic tests are:
- Imaging techniques like CT-scan, PET-scan, MRI, and X-ray.
- Tumor or tumor site biopsy
- Immunohistochemistry
Treatment methods include surgical removal of the tumour, chemotherapy, and radiotherapy.
What support can we give for Malignant Triton Tumor?
Malignant Triton Tumor is a rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. We provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from a rare cancer such as Malignant Triton Tumor, we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways: Donations — Without a Ribbon is grateful when we receive every donation. Giving to Without a Ribbon helps us to provide ongoing support, organise the annual gathering and subsidise the costs of our Warriors attending these conferences. Sponsorship — If you wish to sponsor our charity, please contact us using this form. Volunteering — We are always looking for volunteers to help with different aspects of running our charity. So, if you are looking for volunteer work, please feel free to contact us.
