What is a malignant triton tumor?Malignant triton tumor is a high-grade tumor and the subtype of malignant peripheral nerve sheath tumor. Malignant Triton tumor generally arises from the distant part of the nerves of the head, neck, arms, legs, chest, and abdomen.
What is a malignant peripheral nerve sheath tumor?A malignant peripheral nerve sheath tumor (MPNST) is a type of connective tissue (tissues that bind, separate, or support other tissues or organs) cancer that surrounds the nerves. It is a high-grade tumor and shows a poor prognosis (likely course of the disease). The 5-year survival rate with treatment is 10-14%.
What is a high-grade tumor?A high-grade tumor is a tumor that grows rapidly and spreads to other parts of the body from where it originated.
Disease CausesThere is no well-known cause.
Disease EpidemiologyMalignant triton tumor accounts for approximately 5% of all malignant peripheral nerve sheath tumors (MPNST). It is equally common in both males and females. It can occur at any age but the peak age for the occurrence of the disease is 30 years.
Signs and symptomsThe patient may suffer from the following signs and symptoms. These are
- Malignant Triton tumor generally arises from the distant part of the nerves of the head, neck, arms, legs, chest, and abdomen.
- In very rare cases malignant triton tumors can originate from the brain, heart, lungs, spleen, liver, and buttocks.
- Slowly growing solid mass which is usually painless usually develops at the shoulder, arms, legs, chest, abdomen, or head, and neck region.
DIAGNOSIS AND TREATMENTDiagnostic tests are:
- Imaging techniques like CT-scan, PET-scan, MRI, and X-ray.
- Tumor or tumor site biopsy