What is a Malignant Hemangiopericytoma or Solitary Fibrous Tumour?
Malignant hemangiopericytoma or solitary fibrous tumours belong to the group of benign (non-malignant) or malignant (malignant) soft tissue or mesenchymal tumours. A solitary fibrous tumour usually occurs in the lungs, meninges, and other soft tissues of the body. Malignant solitary fibrous tumours are larger and tend to metastasize (spread of the tumour to other parts of the body from the place of its origin).
Disease Aetiology (Causes)
There is no well-known cause.
Disease Epidemiology
Solitary fibroids accounted for approximately 1-2% of all soft tissue tumours. They mainly develop in adults, whose average age is 45-50 years. They are rare in infants and children.
Signs and Symptoms
Signs and symptoms vary according to the location of the tumour.
Signs and Symptoms of Pleural (Lungs) Solitary Fibrous Tumor / (Pleural SFT)
- Pain in chest
- Cough
- Difficulty in breathing
- Symptoms of Low blood glucose levels (hypoglycemia)
Signs and Symptoms of Solitary Fibrous Tumor Of Limbs (Arms And Legs)
Deep-seated enlarged painless mass in the thigh, armpit or pelvis
Diagnosis
The following diagnostic techniques and procedures can be used to make a diagnosis these are
- Diagnostic imaging techniques such as USG, CT-scan, MRI, and PET scan can be used to detect the site, size, and extent of the tumor.
- Tumor biopsy (FNAC)
- Histopathological examination
- Cytogenetics
Treatment
Surgical resection (surgical removal of the tumour part of the skin along with the removal of some surrounding healthy tissues) of the tumour along with radiation is the main treatment option.
What Support can we Give for Malignant Hemangiopericytoma or Solitary Fibrous Tumour?
Malignant Hemangiopericytoma or Solitary Fibrous Tumour is a rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Malignant Hemangiopericytoma or Solitary Fibrous Tumour we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways: