What is Dermatofibrosarcoma Protuberans?
Dermatofibrosarcoma Protuberance is a rare soft tissue cancer that arises from the deep layers of the skin. It is an aggressive tumour that can invade surrounding tissue but rarely spreads to other parts of the body. It also tends to recur after treatment. The most common sites for dermatofibrosarcoma are the chest and abdomen, but it can also develop in the arms, legs, head, and neck.
Disease Etiology (Causes)
There is no well-known cause. However, certain chromosomal aberrations (changes in chromosomal structure and numbers), trauma or injury, surgical burns, scars, and sites of vaccinations are the risk factors for the development of dermatofibrosarcoma protuberance.
Disease Epidemiology
It accounts for approximately 1% of all soft tissue cancers. The annual incidence is 3 cases per million populations. It is equally common among both the male and female populations. The average age of the disease development is 20-50 years.
Signs and Symptoms
The patient may suffer from the following signs and symptoms. These are
- A slowly growing tumour that appears as a papule (small pimple or swelling on the skin) or a patch that can grow to a lump or mass.
- In advanced cases, it may bleed or ulcerate
Diagnosis
The following diagnostic techniques and procedures can be used to make a diagnosis these are
- Diagnostic imaging techniques such as USG, CT-scan, MRI, and PET scan can be used to detect the site, size, and extent of the tumour.
- Dermoscopy
- Skin biopsy
Treatment
Surgical resection (surgical removal of the tumour part of the skin along with the removal of some surrounding healthy tissues) of the tumour and radiation therapy are the main treatment options.
What Support can we Give for Dermatofibrosarcoma Protuberans?
Dermatofibrosarcoma Protuberans is a rare cancer, meaning it is not as well known as other forms of cancer. Without a Ribbon is an Australian organisation that provides support for individuals who suffer from rare cancers. So, we provide a designated platform for Warriors to obtain information specific to their Rare Cancer. We also provide annual opportunities for our Warriors to meet and learn from each other. If you suffer from rare cancer such as Dermatofibrosarcoma Protuberans we can help and support you through your journey thanks to the generous donations we receive. Click the link below to sign up and become a Warrior today!
You can help us with your donation:
Without a Ribbon is a charity that works hard to aid those who suffer from rare cancers. You can help our cause in a variety of ways:
